Case 16 Bilateral Cleft Lip Deformity
16.1 Description
Bilateral cleft lip deformity
Left side is complete, right incomplete with presence of Simonart’s band
Flattening of nasal tip and widening of nose with shortened columella
Nostrils are asymmetric and wider on left side due to complete cleft
Left alveolar cleft deformity with gap noted between segments
Palate is not visualized
16.2 Work-Up
16.2.1 History
Family history of orofacialclefting
Evidence of feeding difficulties, appropriate weight gain
Monitor for appropriate weight gain
Additional medical problems and associated syndromes
16.2.2 Physical Examination
The examination should focus on four features: Nose, lip, alveolus, and palate
Cleft lip and palate classification
Unilateral versus bilateral
Complete (involvement of nasal floor) versus incomplete
Isolated cleft lip (primary palate) versus cleft lip and palate (primary and secondary palates)
Additional facial dysmorphic features
Lower lip pits: Van der Woude syndrome (autosomal dominant)
Complete physical examination to look for any other anatomic abnormality
Consider possibility of syndromic presentation
16.2.3 Pertinent Imaging or Diagnostic Studies
Echocardiogram, renal ultrasound, skeletal X- rays, etc., depending on physical findings
16.2.4 Consultations
Children with clefts are ideally cared for by multidisciplinary team: Plastic surgery, otolaryngology, speech pathology, audiology, child/developmental psychology, nursing, pediatric dentistry, orthodontics, and oral and maxillofacial surgery.
16.3 Treatment
Management via multidisciplinary team
Schedule of treatment (see Table 15.1 for cleft management timeline)
16.3.1 Feeding: Critical Aspect of Cleft Care
Specialized nipples/bottles: Dr. Brown bottle, Haberman nipple (with a squeezable tip) or Pigeon nipple (with crosscut opening for faster flow)
General principle is to hold infant at 45 degrees and drip formula into the mouth and allow the infant to swallow.
Babies with cleft palate cannot create adequate suction on a bottle or breast.
Weight gain: After the first 2 weeks of life, the child should gain half a pound every week