Morphea (Localized Scleroderma)
Jeffrey P. Callen
(ICD-9 701.0)
Symptoms and Signs
Morphea (localized scleroderma) is an asymptomatic condition limited to the skin. Some patients complain of a tight feeling of their skin, or pruritus or burning. Morphea is a localized hardening of the skin. The condition occurs in three forms—plaques, linear, and generalized. Plaques of morphea are indurated and red to violaceous at the borders (Fig. 66-1). Linear scleroderma has a similar appearance. It occurs on the face, where it is known as “en coup de sabre,” or on the extremities. Facial linear scleroderma may rarely affect underlying tissues including the bones and the brain and is known as Parry–Romberg syndrome. In generalized morphea, the plaques are large and widespread.