Treatment: All patients with Marfan syndrome should be monitored directly by a cardiologist and a cardiothoracic surgeon as needed. Routine echocardiograms and evaluations for aortic aneurysms are required. β-Blockade has been shown to be helpful to decrease mean arterial pressure. This reduces the pressure on the weakened vessel walls and subsequently decreases the likelihood of arterial dilation, dissection, and aneurysms. Calcium channel blockers and angiotensin-converting enzyme (ACE) inhibitors are second-line agents. Patients with Marfan syndrome who are closely followed and treated promptly may live a normal life span. They must be educated to avoid strenuous physical activity and contact sports. Surgery to repair aortic dilation and aneurysm is required once the caliber of the aorta reaches 5.0 cm or if the rate of enlargement is greater than 0.5 cm/year. Ocular disease should be evaluated and treated promptly by an ophthalmologist.
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